Aortopathy Flashcards¶
Q: What is the surgical threshold for Marfan syndrome? A: ≥5.0 cm (Class I); ≥4.5 cm with risk factors (Class IIa) Tags: aortopathy, marfan, surgery, high-yield
Q: What is the surgical threshold for Loeys-Dietz syndrome (TGFBR1/2)? A: ≥4.2 cm Tags: aortopathy, loeys-dietz, surgery, high-yield
Q: What are risk factors for earlier aortic surgery? A: Rapid growth >0.5 cm/year, family history of dissection, planned pregnancy, significant AR Tags: aortopathy, surgery
Q: What is first-line medical therapy for Marfan syndrome? A: Beta-blocker OR ARB (equally effective - both Class I) Tags: aortopathy, marfan, treatment, high-yield
Q: What is preferred medical therapy for Loeys-Dietz syndrome? A: ARB (preferred over beta-blocker) Tags: aortopathy, loeys-dietz, treatment
Q: What defines vascular Ehlers-Danlos syndrome aortic management? A: Most fragile vessels - surgery ONLY for emergencies; avoid unnecessary interventions Tags: aortopathy, veds, high-yield
Q: What screening is required for first-degree relatives of TAA/dissection? A: Aortic imaging (Class I recommendation) Tags: aortopathy, screening, high-yield
Q: What are exercise restrictions for aortopathy patients? A: Avoid intense isometric exercise, burst activities, collision/contact sports Tags: aortopathy, exercise
Q: What is the pre-pregnancy surgical threshold for Marfan? A: >4.5 cm aortic root Tags: aortopathy, pregnancy
Q: When is cesarean section indicated for aortopathy? A: Aortic diameter ≥4.5 cm Tags: aortopathy, pregnancy, delivery